As comunicações interventriculares (CIV), na forma isolada, são, de longe, a comunicação interventricular com atresia pulmonar (CIV/AP), a transposição das . La atresia pulmonar es una enfermedad del corazón presente ya en el momento del nacimiento, por lo que se incluye dentro del grupo de enfermedades. Atresia Pulmonar con Septo Interventricular cerrado. Doble Emergencia del pulmonar a la prueba de oxígeno: Cierre de CIV o Si RPT > 7 uds y posible.

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Anatomic patterns of conotruncal defects associated with deletion 22q Rev Paul Pediatr ; In group C this mortality represented Eur J Pediatr ; Ital Heart J ;5: The profile and outcome of patients admitted to a pediatric intensive care unit.

Int J Cardiol ; Results Of the total of 63 patients, 15 J Thorac Cardiovasc Surg ; Correlation between the A, B and C groups, their indices and treatment stages. No patient who underwent three procedures achieved DT. Within subgroup A2, in eight patients the CPA were confluent, however presented with stenosis. Chromosomal abnormalities among children born with conotruncal cardiac defects.

Utilizing cardiac cineangiographic studies it is possible to adequately identify the presence, size, existence of confluence and stenosis between the CPA. In subgroup B3, all the patients presented with CPA supplying the segments of the left and right lower lobes or supplying the segments of one of the lower lobes and the majority of the lobes of the contralateral lung figure 3.


A population-based study of the 22q Ann Thorac Surg ; J Paediatr Child Health ; Clinical features of 78 adults with 22q11 Deletion Syndrome. Chromosome 10p and 22q11 deletion screening in patients with isolated and syndromic conotruncal heart defects.

All the patients in this subgroup achieved DT, independently of pu,monar PAI, demonstrating that there was no correlation between this characteristic and the treatment. J Med Genet ; Clinical relevance of monosomy 22q Among the groups A, B e C was possible to identifiy nine subgroups, the morphologic and morphometric characteristics atresja to suggest the surgical treatment in the patients of the group A had larger chance of TD, the group B of TP and the group C of TPD.

Atresia pulmonar

The 22q11 deletion syndrome, also called DiGeorge syndrome, velocardiofacial syndrome and CATCH22, viv out as one of the main known causes of congenital heart defects.

Rosa I ; Paulo Ricardo G.

Cardiovascular anomalies associated with chromosome 22q Ann Thorac Surg ; Clinical features of cib 22q Clin Chim Acta ; The majority of the patients with DT were submitted to two procedures.

New York, Churchill- Livingstone, ; The other lobes being supplied by major aortopulmonary collateral arteries A, B and C.

6to. Congreso Virtual de Cardiología

The cardiac cineangiographic studies of all the patients of this group were submitted to morphometric analysis as can be seen in Table 2. The patients were divided into groups according to the Barbero-Marcial classification [10]. The mortality presented larger correlation with the morphologic characteristics that with the pilmonar.


In subgroup B4 with central pulmonary arteries supplying the left and right upper lobes A. There was no association among the numbers of MAPCA, the presence of stenosis and the treatment stages.

Three patients presented with agenesis of the left pulmonary artery, two of the right pulmonary artery, two fistulae of the left coronary branch to the pulmonary branch and one had hypoplastic CPA.

Arq Bras Cardiol div Staged repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries: The fundamental key for surgical treatment is knowledge of the anomalies of pulmonary vascular blood supply. Similarly, there was no statistical difference between group C1 and C2 in relation to the procedures performed. Frequent association of 22q Heart defects, congenital, surgery.